Conference: 2018 PHA International PH Conference & Scientific Sessions
Release Date: 06.28.2018
Presentation Type: Abstracts
File Download: Conference 2018_1033
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Abstract presented at the 2018 International PH Conference and Scientific Sessions in Orlando, Fla., June 28-July 1, 2018.
We report 3 pediatric cases of pulmonary hypertension (PH) whereby digital subtraction angiography (DSA) images provided additional information regarding pulmonary vascular and lung parenchymal pathology compared to traditional angiography.
It is essential to diagnose the etiology of PH in children for appropriate therapy. In a French series by Cottin et al, a 50% prevalence of PH is described with pulmonary fibrosis and emphysema syndrome in adults. In children, especially those with history of prematurity, bronchopulmonary dysplasia is commonly attributed to cause PH. Digital subtraction angiography can provide additional benefits in determining the cause of PH in children.
We reviewed retrospectively the hemodynamic data and DSA findings in 3 pediatric PH cases (Figure).
Table-1 describes the demographics and cardiac hemodynamic data. The DSA images in our patients with PH showed segmental hypoperfusion and abnormal capillary phase suggesting abnormal pulmonary vascularity and parenchymal changes in the setting of reactive PH. [Table]
Digital subtraction angiography can provide additional information compared to traditional angiography in evaluation of PH in selected patients.
Figure 1: DSA findings in case 1-3
Table 1: Summary of PH patients and hemodynamic data